Giant right atrial thrombus unmasking Behçet's disease: A rare cardiovascular manifestation.
Behçet's disease is a systemic vasculitis in which intracardiac thrombus formation is a rare but potentially life-threatening manifestation, predominantly involving the right heart. We report the case of a 37-year-old male presenting with pulmonary embolism associated with extensive central ven…
Rhinologic Manifestations in Systemic Rheumatic Disease.
Sinonasal symptoms are a common early manifestation of several systemic inflammatory diseases and may precede multisystem involvement by days to years. Because nasal obstruction, drainage, epistaxis, crusting, and hyposmia are frequently attributed to chronic rhinosinusitis, diagnoses such as antine…
Choroidal Tuberculosis in Miliary Disease: A Multimodal Imaging Spectrum Across Iatrogenic and Disease-Mediated Immunosuppression.
To describe the multimodal imaging findings of choroidal tuberculosis in two cases of miliary tuberculosis occurring in the setting of distinct forms of immunosuppression. Retrospective analysis of four eyes with miliary choroidal tuberculosis. Case 1 was a young male with newly diagnosed HIV infect…
Research on sleep patterns in individuals with vasculitis remains limited. This SleepVasc study aimed to 1) evaluate sleep disturbances and a range of sleep health dimensions in individuals with vasculitis, and 2) identify potential risk factors for sleep problems/disturbances/disorders. SleepVasc w…
Primary anetoderma as a possible preclinical cutaneous clue of Behçet's disease: evidence suggesting early microvascular-driven dermal elastolysis.
Anetoderma is a rare elastolytic dermatosis characterized by focal loss of dermal elastic fibers leading to localized flaccid, atrophic, or herniated skin lesions. Although it may occur as a primary disorder or secondary to inflammatory dermatoses, infections, or trauma, immune-mediated vascular inj…
Isolated granulomatous pulmonary artery vasculitis associated with Hughes-Stovin syndrome: a case report.
Hughes-Stovin syndrome (HSS) is an exceptionally rare vasculitis, characterized by pulmonary artery aneurysms with in situ thrombosis and is increasingly regarded as part of the vascular Behcet spectrum. Diagnosis remains challenging due to its rarity, lack of validated diagnostic criteria, and over…
Factors Associated with Adalimumab Initiation in Non-Infectious Uveitis: A Propensity Score Matched Analysis.
To identify factors associated with adalimumab initiation in non-infectious uveitis. This was a retrospective case-control study using multicentric data of 3204 patients. The primary outcome was whether adalimumab was initiated, and the secondary outcome was time to initiation. To investigate factor…
Eosinophilic angiocentric fibrosis in paediatric IgG4-related disease.
A girl in the first decade of life presented with a 1.5 year history of gradually progressive bilateral upper eyelid swelling with bilateral proptosis, more prominent on the right side. She had a partial response to oral prednisolone, but symptoms recurred during tapering. Examination showed…